Abatacept for Lung Disease in Common Variable Immunodeficiency

This study is testing a drug called abatacept (also known as Orencia) for people with Common Variable Immunodeficiency (CVID) who also have a type of lung disease called Interstitial Lung Disease (ILD). Abatacept works by blocking certain signals that activate immune cells (T lymphocytes). Currently, there isn't a standard treatment for this condition. Researchers want to see if abatacept can improve lung health compared to a placebo (an inactive substance). You might be able to join if you are at least 4 years old and have a confirmed diagnosis of CVID. The main way they will measure success is by looking at changes in your lungs using a special CT scan after 6 months.

Study design
This is a multi-site, randomized, blinded study comparing abatacept to a placebo, with some participants receiving abatacept openly. It plans to enroll 38 participants, including children and adults.
What's involved
Participants will receive treatment for 12 months, with the option to continue abatacept for up to 3 years. The primary outcome will be measured at 6 months using a High Resolution CT Scan of the chest.
Compensation
Not stated in the trial record.
Follow-up
After the initial 12 months of treatment, patients have the option to continue abatacept for up to 3 years.

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NCT04925375

Abatacept for the Treatment of Common Variable Immunodeficiency With Interstitial Lung Disease

Recruiting
PHASE2Ages 4+InterventionalTreatment
Children's Hospital Medical Center, Cincinnati
~38 participants
Updated 2026-07-22 on ClinicalTrials.gov
What's tested:AbataceptPlacebo

At a glance

Recruiting sites
6 of 6 listed sites are recruiting right now
RecruitingSuspended, closed, or not yet open
What they're measuring
High Resolution CT Scan of the chest (HRCT)
Measured over 6 months
Interstitial Lung Disease
Common Variable Immunodeficiency
6 sites across 6 states
California1
Florida1
Massachusetts1
Minnesota1
North Carolina1
Ohio1
  • Michael Jordan · PRINCIPAL_INVESTIGATOR · Children's Hospital Medical Center, Cincinnati

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Eligibility criteria

Inclusion

Patients must have completed the abatacept for the treatment of Interstitial Lung Disease in Common Variable Immunodeficiency (ABCVILD) trial
Patients must have demonstrated positive response to abatacept.
Patients must provide informed consent to participate in the Extended Treatment Plan.
  • High Resolution CT Scan of the chest (HRCT)6 months

    Proportion of subjects achieving a significant response (defined as \>30 percent change in lung tissue disease burden by GLILD) on HRCT after 6 months of abatacept therapy.