Long-Term Development of Muscular Dystrophy Outcome Assessments

This is an observational study looking at how Limb Girdle Muscular Dystrophy (LGMD), Myotonic Dystrophy Type 2 (DM2), and late-onset Pompe disease (LOPD) progress over 24 months. Researchers want to see if a specific assessment tool, the North Star Assessment for LGMD (NSAD), is a good way to measure changes in these conditions. This will help in developing new treatments faster. You might be able to join if you are between 6 and 50 years old, have weakness consistent with proximal weakness, and have a confirmed genetic diagnosis of LGMD, DM2, or LOPD, with good lung function (FVC above 30%). There are no specific interventions or drugs being tested in this study.

Study design
This is an observational study with a planned enrollment of up to 1000 participants. It is not testing a specific drug or treatment.
What's involved
This is a 24-month study. The primary goal is to explore the suitability and feasibility of the North Star Assessment for LGMD (NSAD) at baseline and 24 months.
Compensation
Not stated in the trial record.
Follow-up
Participants will be followed for 24 months, with measurements taken at baseline and 24 months.

AI-generated from the public study record. Only the study team can confirm whether you're eligible — confirm details with them before making decisions.

NCT05989620

Long-Term Development of Muscular Dystrophy Outcome Assessments

Recruiting
Not specifiedAges 6–50Observational
Virginia Commonwealth University
~1,000 participants
Updated 2025-11-18 on ClinicalTrials.gov

At a glance

Recruiting sites
1 of 1 listed site is recruiting right now
RecruitingSuspended, closed, or not yet open
What they're measuring
To explore the suitability and feasibility of the North Star Assessment for LGMD (NSAD) in the muscular dystrophies
Measured over Baseline to 24 months
LGMD1B
LGMD1C
LGMD1D
LGMD1E
LGMD1F
LGMD1G
LGMD1H
LGMD2A
LGMD2B
LGMD2C
LGMD2D
LGMD2E
LGMD2F
LGMD2G
LGMD2I
LGMD2J
LGMD2K
LGMD2L
LGMD2M
LGMD2N
LGMD2O
LGMD2P
LGMD2Q
LGMD2S
LGMD2T
LGMD2U
LGMD2W
LGMD2X
LGMD2Y

NCT05989620

Where you'd take part

This study runs at 1 site. They're the same protocol — you choose where, and that choice sets who your contact draft is addressed to.

  • Virginia Commonwealth University

    Richmond, Virginiastudy coordinator listed

    Recruiting

Sites open and close at different times, so the status above is per site — it can differ from the study's overall status.

  • Nicholas Johnson, MD · PRINCIPAL_INVESTIGATOR · Virginia Commonwealth University

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  • To explore the suitability and feasibility of the North Star Assessment for LGMD (NSAD) in the muscular dystrophiesBaseline to 24 months

    The NSAD is a functional scale specifically designed to measure motor performance in individuals with LGMD. It consists of 29 items that are considered clinically relevant items from the adapted North Star Ambulatory Assessment and the Motor Function Measure 20 with a maximum score of 54.