JAG201 Gene Therapy for SHANK3 Haploinsufficiency

This study is testing a gene therapy called JAG201 for children and adults with SHANK3 haploinsufficiency, including those with Phelan-McDermid Syndrome. JAG201 is a special virus (Adeno-associated virus 2/9) that delivers a miniature version of the human SHANK3 gene. The main goal of this study is to see if JAG201 is safe and well-tolerated. Researchers will also look for any early signs that the treatment is working. You may be able to join if you are between 2 and 9 years old and have a confirmed SHANK3 genetic change and developmental delays. The study is currently enrolling a small number of participants, with a planned enrollment of 6 children first.

Study design
This is a Phase 1/2, first-in-human, open-label study, meaning everyone knows what treatment is being given. It aims to enroll a target of 6 pediatric participants aged 2 to 9 years.
What's involved
You would undergo pre-screening and screening for up to 90 days, receive a one-time injection of JAG201, and then have regular follow-up visits for safety and clinical activity assessments.
Compensation
Not stated in the trial record.
Follow-up
Participants will be followed for safety and tolerability for at least 5 years after receiving the JAG201 treatment.

AI-generated from the public study record. Only the study team can confirm whether you're eligible — confirm details with them before making decisions.

NCT06662188

JAG201 Gene Therapy Study in Children & Adults With SHANK3 Haploinsufficiency

Recruiting
PHASE1Ages 2–9InterventionalTreatment
Jaguar Gene Therapy, LLC
~6 participants
Updated 2026-09-03 on ClinicalTrials.gov
What's tested:JAG201

At a glance

Recruiting sites
3 of 3 listed sites are recruiting right now
RecruitingSuspended, closed, or not yet open
What they're measuring
Incidence of Adverse Events (AEs)
Measured over Enrollment to Month 60
+3 more outcomes measured
SHANK3 Haploinsufficiency
Phelan-McDermid Syndrome

NCT06662188

Where you'd take part

This study runs at 3 sites. They're the same protocol — you choose where, and that choice sets who your contact draft is addressed to.

  • Boston Children's Hospital

    Boston, Massachusettsstudy coordinator listed

    Recruiting

  • Rush University

    Chicago, Illinoisstudy coordinator listed

    Recruiting

  • Seaver Autism Center at Mount Sinai

    New York, New Yorkstudy coordinator listed

    Recruiting

Sites open and close at different times, so the status above is per site — it can differ from the study's overall status.

  • Dan Gallo, PhD · STUDY_DIRECTOR · Jaguar Gene Therapy

Opens a ready-to-send draft in your own email app — review before sending.

  • Incidence of Adverse Events (AEs)Enrollment to Month 60

    Incidence, type, severity, and frequency of AEs

  • Incidence of Serious Adverse Events (SAEs)Enrollment to Month 60

    Incidence, type, severity, and frequency of SAEs

  • Clinically significant abnormalities in laboratory valuesEnrollment to Month 60

    Changes in clinically significant abnormalities in laboratory values

  • Incidence of immunogenicity response abnormalitiesEnrollment to Month 60

    Incidence of anti-AAV9 antibodies, anti-transgene antibodies, and T-cell reactivity to transgene over time